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產品名稱:原纖維蛋白1抗體,Anti-FBN1/fibrillin 1*
中文名稱:原纖維蛋白1抗體
英文名稱:Anti-FBN1/fibrillin 1
產品編號:BYK-1157R
產品別名: fibrillin1; 350 kDa glycoprotein component extracellular microfibril; FBN 1; FBN; Fibrillin 15; Fibrillin15; Marfan syndrome; MASS; MFS 1; MFS1; OCTD; SGS; Weill Marchesani syndrome; WMS; AI536462; B430209H23; Fib-1; Fibrilin-1.
本公司另供應“原纖維蛋白1抗體”的標記有:Alexa Fluor 350 Alexa Fluor 488 Alexa Fluor 555 Alexa Fluor 647 AP APC Biotin Cy3 Cy5 Cy5.5 Cy7 FITC Gold HRP PE PE-Cy3 PE-CY5 PE-CY5.5 PE-CY7 RBITC.
產品規格:100ug/200ug
產品濃度: 1mg/1ml
抗體來源:兔源、鼠源、山羊
克 隆:單克隆抗體、多克隆抗體
抗體類型:一抗
性 狀: 凍干粉或液體
保存條件:Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
原纖維蛋白1抗體,Anti-FBN1/fibrillin 1*技術說明,產品*,由于篇幅原因,更多信息請:
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產品介紹:
Fibrillin is the major constitutive element of extracellular microfibrils and has widespread distribution in both elastic and nonelastic connective tissue throughout the body. The cDNA was identified in 1991 and was mapped coincident with the locus for Marfan syndrome. Subsequent studies confirmed that mutations in the Fibrillin 1 gene are the major cause of Marfan syndrome. The connective tissue protein has a widespread distribution in the connective tissue matrices of skin, lung, kidney, vasculature, cartilage, tendon, muscle, cornea, and ciliary zonule.
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